Staged surgical treatment of brachioplexopathy in an adolescent with Klippel-Feil syndrome: a rare clinical case and literature review

نویسندگان

چکیده

Klippel-Feil syndrome is a congenital malformation, the leading component of which violation segmentation cervical vertebral bodies. The can be combined with other skeletal anomalies: skull asymmetry, scoliosis, high shoulder blades, and ribs. Treatment usually symptomatic; indications for surgical treatment are progressive neurological disorders persistent pain syndrome, develop due to instability unblocked segments, or neurogenic pain. A clinical case 17-year-old patient who developed picture severe upper limb monoparesis during three years compression brachial plexus associated ribs presented. Decompression was performed, led rapid relief gradual partial regression motor disorders. Due incomplete restoration gripping function, tendon-muscle plasty right hand significantly improved possibility self-care. results radiation staged neurophysiological studies described, as well review literature on syndrome.

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ژورنال

عنوان ژورنال: ???????? ????????????

سال: 2021

ISSN: ['2077-7566', '2412-9461']

DOI: https://doi.org/10.14531/ss2021.1.6-13